Classical presentation of Darier's disease: a rare disorder of keratinisation.
نویسندگان
چکیده
Keratosis follicularis or Darier's disease (DD), a rare autosomal dominant disorder is characterised clinically by appearance of multiple, prurutic, discrete, scaly papules affecting seborrheic areas coupled with palmar pits, nail changes and mucosal involvement. Histologicaly the lesions show suprabasal clefts with acantholytic and dyskeratotic cells. We report a case of 35 years old woman with typical clinical and histological features of Darier's disease.
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ورودعنوان ژورنال:
- Journal of Ayub Medical College, Abbottabad : JAMC
دوره 22 3 شماره
صفحات -
تاریخ انتشار 2010